A Manually Curated Knowledgebase of Aging across a variety of Species

Details


Name LMNA G608G
Type somatic mutation
Species Homo sapiens
Tissue skin tissue
Experiment Method qPCR,Western blot,ChIP
Up/Down Up
Pro/Anti Pro
Funtion Description 90% of HGPS cases carry the LMNA G608G (GGC>GGT) mutation within exon 11 of LMNA, activating a splice donor site that results in production of a dominant negative form of lamin A protein, denoted progerin. Our findings demonstrate that progerin expression
Regulation Gene LMNA
Year 2007
Pubmed ID 18060063
Title The mutant form of lamin A that causes Hutchinson-Gilford progeria is a biomarker of cellular aging in human skin.
Drug NA
Disease HGPS
Environment Factors NA
Circulating NA
Variant NA
High-throughput NA