A Manually Curated Knowledgebase of Aging across a variety of Species

Details


Name NA
Type somatic mutation
Species Homo sapiens
Tissue blood samples
Experiment Method qPCR
Up/Down NA
Pro/Anti Pro
Funtion Description The LMNA mutation that caused LCPS in this family is a heterozygous c.899A>G (p.D300G) mutation predicted to alter the coiled-coil domain of lamin A/C. In skin fibroblasts isolated from the proband, the processing and levels of lamin A and C are normal. H
Regulation Gene LMNA
Year 2013
Pubmed ID 23666920
Title LMNA-associated cardiocutaneous progeria: an inherited autosomal dominant premature aging syndrome with late onset
Drug NA
Disease Hutchinson-Gilford progeria syndrome
Environment Factors NA
Circulating 1
Variant somatic mutation
High-throughput NA