A Manually Curated Knowledgebase of Aging across a variety of Species

Details


Name Lmna R225X
Type miRNA
Species Rat
Tissue NA
Experiment Method gene knockout
Up/Down Up
Pro/Anti Pro
Funtion Description The mechanism of LMNA nonsense mutation induced cardiac conduction defects through AV node fibrosis is due to upregulated ECM gene expression upon activation of cardiac apoptosis.
Regulation Gene Lmna R225X
Year 2020
Pubmed ID 31668660
Title Expression of Lmna-R225X nonsense mutation results in dilated cardiomyopathy and conduction disorders (DCM-CD) in mice: Impact of exercise training.
Drug NA
Disease DCM
Environment Factors NA
Circulating NA
Variant NA
High-throughput null